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alpha-Galactosidase A/GLA Antibody

Novus Biologicals, part of Bio-Techne | Catalog # H00002717-D01

Novus Biologicals, part of Bio-Techne
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H00002717-D01

Key Product Details

Species Reactivity

Human

Applications

Immunocytochemistry/ Immunofluorescence, Immunoprecipitation, Western Blot

Label

Unconjugated

Antibody Source

Polyclonal Rabbit IgG

Concentration

This product is unpurified. The exact concentration of antibody is not quantifiable.

Product Specifications

Immunogen

GLA (NP_000160.1, 1 a.a. - 429 a.a.) full-length human protein. MQLRNPELHLGCALALRFLALVSWDIPGARALDNGLARTPTMGWLHWERFMCNLDCQEEPDSCISEKLFMEMAELMVSEGWKDAGYEYLCIDDCWMAPQRDSEGRLQADPQRFPHGIRQLANYVHSKGLKLGIYADVGNKTCAGFPGSFGYYDIDAQTFADWGVDLLKFDGCYCDSLENLADGYKHMSLALNRTGRSIVYSCEWPLYMWPFQKPNYTEIRQYCNHWRNFADIDDSWKSIKSILDWTSFNQERIVDVAGPGGWNDPDMLVIGNFGLSWNQQVTQMALWAIMAAPLFMSNDLRHISPQAKALLQDKDVIAINQDPLGKQGYQLRQGDNFEVWERPLSGLAWAVAMINRQEIGGPRSYTIAVASLGKGVACNPACFITQLLPVKRKLGFYEWTSRLRSHINPTGTVLLQLENTMQMSLKDLL

Clonality

Polyclonal

Host

Rabbit

Isotype

IgG

Scientific Data Images for alpha-Galactosidase A/GLA Antibody

Western Blot: alpha-Galactosidase A/GLA Antibody [H00002717-D01]

Western Blot: alpha-Galactosidase A/GLA Antibody [H00002717-D01]

Western Blot: alpha-Galactosidase A/GLA Antibody [H00002717-D01] - Expression in transfected 293T cell line. Lane 1: GLA transfected lysate(48.8 KDa). Lane 2: Non-transfected lysate.
Western Blot: alpha-Galactosidase A/GLA Antibody [H00002717-D01]

Western Blot: alpha-Galactosidase A/GLA Antibody [H00002717-D01]

Western Blot: alpha-Galactosidase A/GLA Antibody [H00002717-D01] - Expression in HeLa.
Immunoprecipitation: alpha-Galactosidase A/GLA Antibody [H00002717-D01]

Immunoprecipitation: alpha-Galactosidase A/GLA Antibody [H00002717-D01]

Immunoprecipitation: alpha-Galactosidase A/GLA Antibody [H00002717-D01] - GLA transfected lysate using anti-GLA MaxPab rabbit polyclonal antibody and Protein A Magnetic Bead (U0007), and immunoblotted with GLA purified MaxPab mouse polyclonal antibody.

Applications for alpha-Galactosidase A/GLA Antibody

Application
Recommended Usage

Immunoprecipitation

1:10-1:500

Western Blot

1:100-1:2000
Application Notes
This antibody is useful for Western Blot, Immunoprecipitation
Please Note: Optimal dilutions of this antibody should be experimentally determined.

Formulation, Preparation, and Storage

Purification

Unpurified

Formulation

No additive

Preservative

No Preservative

Concentration

This product is unpurified. The exact concentration of antibody is not quantifiable.

Shipping

The product is shipped with polar packs. Upon receipt, store it immediately at the temperature recommended below.

Stability & Storage

Aliquot and store at -20C or -80C. Avoid freeze-thaw cycles.

Background: alpha-Galactosidase A/GLA

This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]

Alternate Names

Agalsidase alpha, GALA, Melibiase

Gene Symbol

GLA

Additional alpha-Galactosidase A/GLA Products

Product Documents for alpha-Galactosidase A/GLA Antibody

Certificate of Analysis

To download a Certificate of Analysis, please enter a lot number in the search box below.

Product Specific Notices for alpha-Galactosidase A/GLA Antibody

This product is produced by and distributed for Abnova, a company based in Taiwan.

This product is for research use only and is not approved for use in humans or in clinical diagnosis. Primary Antibodies are guaranteed for 1 year from date of receipt.

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