LYAG/GAA Antibody (3C6)

Novus Biologicals, part of Bio-Techne | Catalog # H00002548-M01

Novus Biologicals, part of Bio-Techne
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Key Product Details

Species Reactivity

Human

Applications

ELISA, Western Blot

Label

Unconjugated

Antibody Source

Monoclonal Mouse IgG1 kappa Clone # 3C6

Concentration

Concentrations vary lot to lot. See vial label for concentration. If unlisted please contact technical services.

View all Lysosomal alpha-Glucosidase Antibodies »

Product Specifications

Immunogen

GAA (AAH40431, 851 a.a. ~ 952 a.a) partial recombinant protein with GST tag. MW of the GST tag alone is 26 KDa. GEARGELFWDDGESLEVLERGAYTQVIFLARNNTIVNELVRVTSEGAGLQLQKVTVLGVATAPQQVLSNGVPVSNFTYSPDTKVLDICVSLLMGEQFLVSWC

Localization

Lysosome

Specificity

GAA - glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II)

Clonality

Monoclonal

Host

Mouse

Isotype

IgG1 kappa

Description

Quality control test: Antibody Reactive Against Recombinant Protein.

Scientific Data Images for LYAG/GAA Antibody (3C6)

Western Blot: LYAG/GAA Antibody (3C6) [H00002548-M01]

Western Blot: LYAG/GAA Antibody (3C6) [H00002548-M01]

Western Blot: LYAG/GAA Antibody (3C6) [H00002548-M01] - Western Blot detection against Immunogen (36.96 KDa)
ELISA: LYAG/GAA Antibody (3C6) [H00002548-M01]

ELISA: LYAG/GAA Antibody (3C6) [H00002548-M01]

ELISA: LYAG/GAA Antibody (3C6) [H00002548-M01] - Detection limit for recombinant GST tagged GAA is 0.3 ng/ml as a capture antibody.

Applications for LYAG/GAA Antibody (3C6)

Application
Recommended Usage

Western Blot

1:500
Application Notes
Antibody reactivity against Recombinant Protein with GST tag on ELISA and WB. GST tag alone is used as a negative control.

Formulation, Preparation, and Storage

Purification

IgG purified

Formulation

In 1x PBS, pH 7.4

Preservative

No Preservative

Concentration

Concentrations vary lot to lot. See vial label for concentration. If unlisted please contact technical services.

Shipping

The product is shipped with polar packs. Upon receipt, store it immediately at the temperature recommended below.

Stability & Storage

Aliquot and store at -20C or -80C. Avoid freeze-thaw cycles.

Background: Lysosomal alpha-Glucosidase

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

Long Name

Glucosidase, Alpha; Acid

Alternate Names

Acid alpha-Glucosidase, Acid Maltase, GAA, LYAG, Lysosomal alphaGlucosidase

Entrez Gene IDs

2548 (Human)

Gene Symbol

GAA

OMIM

232 (Human)

UniProt

AAH40431 (Human)

Additional Lysosomal alpha-Glucosidase Products

Product Documents for LYAG/GAA Antibody (3C6)

Product Datasheets

Certificate of Analysis

To download a Certificate of Analysis, please enter a lot number in the search box below.

Download SDS

Product Specific Notices for LYAG/GAA Antibody (3C6)

This product is produced by and distributed for Abnova, a company based in Taiwan.

This product is for research use only and is not approved for use in humans or in clinical diagnosis. Primary Antibodies are guaranteed for 1 year from date of receipt.

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