LYAG/GAA Antibody (SR1086)

Novus Biologicals, part of Bio-Techne | Catalog # NBP3-22335

Recombinant Monoclonal Antibody
Novus Biologicals, part of Bio-Techne
Catalog #
Availability
Size / Price
Qty
NBP3-22335-50ul
NBP3-22335-100ul
Print Quote
Bulk Order
100% Guarantee

Key Product Details

Species Reactivity

Human, Mouse, Rat

Applications

Western Blot

Label

Unconjugated

Antibody Source

Recombinant Monoclonal Rabbit IgG Clone # SR1086

Concentration

Please see the vial label for concentration. If unlisted please contact technical services.

View all Lysosomal alpha-Glucosidase Antibodies »

Product Specifications

Immunogen

A synthesized peptide derived from human LYAG/GAA (Uniprot #: P10253)

Specificity

Detects endogenous levels of total LYAG/GAA

Clonality

Monoclonal

Host

Rabbit

Isotype

IgG

Scientific Data Images for LYAG/GAA Antibody (SR1086)

Western Blot: LYAG/GAA Antibody (SR1086) [NBP3-22335] -

Western Blot: LYAG/GAA Antibody (SR1086) [NBP3-22335] - Western blot analysis using NBP3-22335 in Human fetal liver lysate.

Applications for LYAG/GAA Antibody (SR1086)

Application
Recommended Usage

Western Blot

1:500-1:2000
Please Note: Optimal dilutions of this antibody should be experimentally determined.

Formulation, Preparation, and Storage

Purification

Affinity purified

Formulation

PBS, pH 7.4, 150mM NaCl, 50% glycerol.

Preservative

0.02% Sodium Azide

Concentration

Please see the vial label for concentration. If unlisted please contact technical services.

Shipping

The product is shipped with polar packs. Upon receipt, store it immediately at the temperature recommended below.

Stability & Storage

Store at 4C short term. Aliquot and store at -20C long term. Avoid freeze-thaw cycles.

Background: Lysosomal alpha-Glucosidase

GAA encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq]

Long Name

Glucosidase, Alpha; Acid

Alternate Names

Acid alpha-Glucosidase, Acid Maltase, GAA, LYAG, Lysosomal alphaGlucosidase

Gene Symbol

GAA

Additional Lysosomal alpha-Glucosidase Products

Product Documents for LYAG/GAA Antibody (SR1086)

Product Datasheets

Certificate of Analysis

To download a Certificate of Analysis, please enter a lot number in the search box below.

Download SDS

Product Specific Notices for LYAG/GAA Antibody (SR1086)

This product is for research use only and is not approved for use in humans or in clinical diagnosis. Primary Antibodies are guaranteed for 1 year from date of receipt.

Privacy and Cookie Policy
Site Map
© Copyright 2024 Bio-Techne. All Rights Reserved.