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DBT Products

The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq]
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42 results for "DBT" in Products

42 results for "DBT" in Products

DBT Products

The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq]
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Applications: IHC, WB, ICC/IF
Reactivity: Human, Mouse, Rat
Applications: IHC, WB, ICC/IF
Reactivity: Human, Mouse, Rat
Applications: IHC, WB
Reactivity: Human
Applications: IHC, WB
Reactivity: Human
Applications: IHC, WB, ICC/IF
Reactivity: Human, Mouse, Rat
Applications: WB, ELISA, ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: WB
Applications: AC
Applications: AC
Applications: AC
Applications: WB, ICC/IF, Flow, CyTOF-ready
Reactivity: Human, Mouse, Rat
Applications: WB, ICC/IF, Flow, CyTOF-ready
Reactivity: Human, Mouse, Rat
Applications: WB, ICC/IF, Flow, CyTOF-ready
Reactivity: Human, Mouse, Rat
Applications: WB, ICC/IF, Flow, CyTOF-ready
Reactivity: Human, Mouse, Rat
Applications: WB, ICC/IF, Flow, CyTOF-ready
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: ICC/IF, Flow
Reactivity: Human, Mouse, Rat
Applications: WB, ICC/IF, Flow, CyTOF-ready
Reactivity: Human, Mouse, Rat
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